Challenges in early diagnosis of juvenile dermatomyositis: a brief review of the literature and a case study
https://doi.org/10.29039/1992-6499-2023-1-106-115
Abstract
Juvenile dermatomyositis (JDM) is an autoimmune, relatively rare multisystem disease of unknown etiology, of which late diagnosis and late initiation of therapy can lead to a child's disability and even lethal outcome. The disease begins in most cases at the age of 5–12 years though can manifest itself both in earlier, and at more advanced age. This disease has a pronounced clinical polymorphism, which complicates early diagnosis and therapy. The article provides a brief overview of research carried out in recent years. A rare case of development of juvenile dermatomyositis in a teenager is considered. Attention is drawn to the complexity of staging this disease during the initial treatment for medical care. A positive dynamics of the course of the disease was shown against the background of correctly selected therapy. The importance of adherence to the prescribed treatment is indicated, the refusal of which can lead to adverse outcomes.
Keywords
juvenile dermatomyositis,
diagnosis,
disease outcomes,
treatment,
dynamic observation,
disease outcomes
Supporting agencies: The authors declare that there is no external funding for the exploration and analysis work
About the Authors
S. N. Mamedova
Azerbaijan Medical University
Azerbaijan
Azerbaijan
Sevda N. Mamedova, Cand. Sci. (Med.), Associate Professor
Baku
S. urkhay N. Musaev
Azerbaijan Medical University
Azerbaijan
Azerbaijan
Surkhay N. Musaev, Dr. Sci. (Med.), Professor
Baku
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For citations:
Mamedova S.N., Musaev S.u. Challenges in early diagnosis of juvenile dermatomyositis: a brief review of the literature and a case study. Astrakhan medical journal. 2023;18(1):106-115. (In Russ.) https://doi.org/10.29039/1992-6499-2023-1-106-115
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