astmedАстраханский медицинский журналAstrakhan medical journal1992-6499ФГБОУ ВО Астраханский ГМУ Минздрава России10.29039/1992-6499-2023-1-106-115astmed-241Research ArticleНАБЛЮДЕНИЯ ИЗ ПРАКТИКИOBSERVATIONS FROM PRACTICEТрудности ранней диагностики ювенильного дерматомиозита: краткий обзор литературы и клинический случайChallenges in early diagnosis of juvenile dermatomyositis: a brief review of the literature and a case studyМамедоваС. Н.MamedovaS. N.

Севда Насреддиновна Мамедова, кандидат медицинских наук, доцент, заведующая отделением

кафедра детских болезней

Учебно-терапевтическая клиника

кардиоревматологическое отделение

Баку

Sevda N. Mamedova, Cand. Sci. (Med.), Associate Professor

Baku

dr.sevda.mammadova@mail.ruМусаевС. Н.MusaevS. Urkhay N.

Сурхай Новрузович Мусаев. доктор медицинских наук, профессор

кафедра детских болезней

Баку

Surkhay N. Musaev, Dr. Sci. (Med.), Professor

Baku

surxaymusayev@gmail.comАзербайджанский медицинский университетАзербайджанAzerbaijan Medical UniversityAzerbaijan202301052023181106115Copyright © Мамедова С.Н., Мусаев С.Н., 20232023Мамедова С.Н., Мусаев С.Н.Mamedova S.N., Musaev S.u.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.astmedj.ru/jour/article/view/241

   Ювенильный дерматомиозит – аутоиммунное, относительно редкое мультисистемное заболевание неизвестной этиологии, позднее установление диагноза и позднее начало терапии которого может привести к инвалидизации ребенка и даже к летальному исходу. Заболевание начинается в большинстве случаев в возрасте 5–12 лет, хотя может дебютировать как в более раннем, так и в более старшем возрасте. Ювенильный дерматомиозит имеет выраженный клинический полиморфизм, что затрудняет своевременную диагностику и терапию. Рассмотрен случай развития этого заболевания у подростка, обращено внимание на сложность постановки диагноза при первичном обращении за медицинской помощью. Показана положительная динамика течения заболевания на фоне верно подобранной терапии. Указано на важность соблюдения предписанного лечения, отказ от которого может привести к неблагоприятному исходу.

   Juvenile dermatomyositis (JDM) is an autoimmune, relatively rare multisystem disease of unknown etiology, of which late diagnosis and late initiation of therapy can lead to a child's disability and even lethal outcome. The disease begins in most cases at the age of 5–12 years though can manifest itself both in earlier, and at more advanced age. This disease has a pronounced clinical polymorphism, which complicates early diagnosis and therapy. The article provides a brief overview of research carried out in recent years. A rare case of development of juvenile dermatomyositis in a teenager is considered. Attention is drawn to the complexity of staging this disease during the initial treatment for medical care. A positive dynamics of the course of the disease was shown against the background of correctly selected therapy. The importance of adherence to the prescribed treatment is indicated, the refusal of which can lead to adverse outcomes.

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The authors declare that there are no conflicts of interest present.